Skip Navigation



BJA Advance Access published online on September 26, 2006
British Journal of Anaesthesia, doi:10.1093/bja/ael251
This Article
Right arrow Full Text (PDF)
Right arrow All Versions of this Article:
97/5/701    most recent
ael251v1
Right arrow E-Letters: Submit a response to the article
Right arrow Alert me when this article is cited
Right arrow Alert me when E-letters are posted
Right arrow Alert me if a correction is posted
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to My Personal Archive
Right arrow Download to citation manager
Right arrowRequest Permissions
Right arrow Disclaimer
Google Scholar
Right arrow Articles by Tumolo, M.
Right arrow Articles by Silvestri, G.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Tumolo, M.
Right arrow Articles by Silvestri, G.
Social Bookmarking
Add to CiteULike   Add to Connotea   Add to Del.icio.us  
What's this?

© The Board of Management and Trustees of the British Journal of Anaesthesia 2006. All rights reserved. For Permissions, please e-mail: journals.permissions@oxfordjournals.org
Accepted July 13, 2006

Case Report

Anaesthetic management of a child with fibrodysplasia ossificans progressiva

M. Tumolo 1 *, A. Moscatelli 1, and G. Silvestri 1

1 Department of Anaesthesia and Intensive Care, Giannina Gaslini Children's Hospital, Largo Gerolamo Gaslini 5, 16147 Genova Quarto, Italy

* To whom correspondence should be addressed.
M. Tumolo, E-mail: miriamtumolo{at}virgilio.it


  Abstract

Fibrodysplasia Ossificans Progressiva (FOP) is a rare inherited disease in which progressive ossification of striated muscles leads to severe disability and respiratory impairment early in life and there are associated characteristic congenital skeletal malformations. Although this condition may prove demanding for the anaesthetist, few reports are available regarding anaesthesia in paediatric patients. We review the clinical features of the disease relevant to anaesthesia and describe the perioperative care of an 18-month-old boy with FOP who underwent endoscopic third-ventriculostomy for hydrocephalus associated with a brainstem mass. We emphasize the importance of an appropriate anaesthetic management of these patients, as inadequate care may lead to exacerbation of the disease with permanent sequelae.

Keywords: anaesthesia, paediatric; complications, intubation tracheal; equipment, bronchoscope; fibrodysplasia ossificans progressiva.
Add to CiteULike CiteULike   Add to Connotea Connotea   Add to Del.icio.us Del.icio.us    What's this?


This article has been cited by other articles:


Home page
 Anesth. Analg.Home page
P. Schober, R. Krage, D. Thone, S. A. Loer, and L. A. Schwarte
Ultrasound-Guided Ankle Block in Stone Man Disease, Fibrodysplasia Ossificans Progressiva
Anesth. Analg., September 1, 2009; 109(3): 988 - 990.
[Abstract] [Full Text] [PDF]

Home page
 JBJSHome page
R. E. Moore, J. P. Dormans, D. S. Drummond, E. M. Shore, F. S. Kaplan, and J. D. Auerbach
Chin-on-Chest Deformity in Patients with Fibrodysplasia Ossificans Progressiva. A Case Series
J. Bone Joint Surg. Am., June 1, 2009; 91(6): 1497 - 1502.
[Full Text] [PDF]


Disclaimer: Please note that abstracts for content published before 1996 were created through digital scanning and may therefore not exactly replicate the text of the original print issues. All efforts have been made to ensure accuracy, but the Publisher will not be held responsible for any remaining inaccuracies. If you require any further clarification, please contact our Customer Services Department.